PT -期刊文章盟Anh-Thu非政府组织Vu AU -埃里森·威利斯AU -佩德罗Gonzalez-Alegre盟迪伦蒂博TI -流行病学的美国少年亨廷顿氏舞蹈症(P2.014) DP - 2017年4月18日TA -神经病学PG - P2.014 VI - 88 IP - 16补充4099 - //www.ez-admanager.com/content/88/16_Supplement/P2.014.short 首页4100 - //www.ez-admanager.com/content/88/16_Supplement/P2.014.full所以Neurology2017 4月18日;88 AB -目的:本研究的目的是描述与亨廷顿氏舞蹈症住院儿童的人口统计和比较结果,如其他住院死亡率和住院时间的控制。背景:少年亨廷顿氏舞蹈症(JHD)典型表现为早期的认知和行为变化,帕金森症,口咽障碍和癫痫发作。没有发表之前的研究评估这些患者的住院治疗的结果。设计/方法:使用行政数据从孩子们的住院数据库(孩子),全国all-payer从儿科住院管理数据的数据库,我们确定了一群JHD患者和对照组的所有其他孩子没有JHD住院。使用抽样权重,我们进行了连续横断面分析2003 - 2009年的孩子住院5 - 20岁儿童被ICD-9代码亨廷顿氏舞蹈症。我们收集统计信息,确定风险诊断,并确定放电处理。我们建立了逻辑回归模型来确定死亡的相对优势和其他放电性情JHD人口控制的孩子相比没有JHD的诊断。结果:我们发现了一个加权和JHD共有271人住院的儿童。最常见的风险诊断癫痫,癫痫持续状态和癫痫。最常见的程序是经皮内镜胃造口术。超过1/3的JHD患者精神障碍诊断代码,主要是情绪障碍。 Length of stay was nearly twice as long as that of controls (7 days vs. 3.75 days, p<0.0002) and they were significantly more likely to die during hospitalization (OR 8.03, p<0.0001). They also had more discharges to another facility (OR 2.93, p<0.0001) or to home health care (OR 4.44, p<0.0001).Conclusions: JHD patients have longer hospitalizations and more complex needs after discharge compared to other hospitalized controls. This study also confirms some of the clinical features of JHD previously described in the literature.Disclosure: Dr. Vu has nothing to disclose. Dr. Willis has nothing to disclose. Dr. Gonzalez-Alegre has received licensing fee payments from Spark Therapeutics. Dr. Thibault has nothing to disclose.

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